Test ID LSDS Lysosomal Disorders Screen, Random, Urine
Ordering Guidance
This test is the recommended screening test for the initial workup of a suspected lysosomal disorder (LD) when the patient's clinical features are not suggestive of any specific LD.
Necessary Information
1. Patient's age is required.
2. Biochemical Genetics Patient Information (T602) is recommended. This information aids in providing a more thorough interpretation of results. Send information with specimen.
Specimen Required
Patient Preparation:
1. Do not administer low-molecular weight heparin before specimen collection.
2. Baby wipes or wipes containing soaps or lotions should not be used before specimen collection because these may interfere with results.
Supplies: Urine Container, 60 mL (T313)
Container/Tube: Clean, plastic urine container with no metal cap or glued insert
Specimen Volume: 12 mL
Pediatric Volume: 3.5 mL
Collection Instructions:
1. Collect a random urine specimen (early morning preferred).
2. No preservative.
Forms
1. Biochemical Genetics Patient Information (T602)
2. If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.
Secondary ID
606771Useful For
Screening patients suspected of having a lysosomal disorder
Testing Algorithm
For information see:
-Lysosomal Disorders Diagnostic Algorithm, Part 1
-Lysosomal Disorders Diagnostic Algorithm, Part 2
-Lysosomal Disorders Screen Interpretive Algorithm
-Epilepsy: Unexplained Refractory and/or Familial Testing Algorithm
Special Instructions
Specimen Type
UrineSpecimen Stability Information
| Specimen Type | Temperature | Time |
|---|---|---|
| Urine | Refrigerated (preferred) | 15 days |
| Frozen | 90 days |
Reject Due To
All specimens will be evaluated at Mayo Clinic Laboratories for test suitability.Reference Values
Dermatan Sulfate:
≤1.00 mg/mmol creatinine
Heparan Sulfate:
≤4 years: ≤0.50 mg/mmol creatinine
≥5 years: ≤0.25 mg/mmol creatinine
Chondroitin-6 Sulfate:
≤24 months: ≤10.00 mg/mmol creatinine
25 months-10 years: ≤2.50 mg/mmol creatinine
≥11 years: ≤1.50 mg/mmol creatinine
Keratan Sulfate:
≤12 months: ≤2.00 mg/mmol creatinine
13-24 months: ≤1.50 mg/mmol creatinine
25 months-4 years: ≤1.00 mg/mmol creatinine
5-18 years: ≤0.50 mg/mmol creatinine
≥19 years: ≤0.30 mg/mmol creatinine
Free Sialic Acid:
≤4 weeks: ≤208 mmol/mol creatinine
5 weeks-12 months: ≤104 mmol/mol creatinine
13 months-18 years: ≤100 mmol/mol creatinine
≥19 years: ≤38 mmol/mol creatinine
Total Sialic Acid:
≤4 weeks: ≤852 mmol/mol creatinine
5 weeks-12 months: ≤656 mmol/mol creatinine
13 months-18 years: ≤335 mmol/mol creatinine
≥19 years: ≤262 mmol/mol creatinine
Total/Free Ratio:
≤4 weeks: 1.94-18.68
5 weeks-12 months: 2.34-13.85
13 months-18 years: 2.63-9.18
≥19 years: 3.35-15.81
Ceramide Trihexosides:
Negative
Sulfatides:
Negative
Oligosaccharides:
Negative
An interpretive report will be provided.
Day(s) Performed
Varies
Report Available
8 to 14 daysPerforming Laboratory
Mayo Clinic Laboratories in Rochester
CPT Code Information
83789
83864
84377
84275